Affiliation:
1. Brazilian Dental Association
2. University of Brasília
3. UnB
Abstract
Williams-Beuren syndrome (WBS) is a rare genetic condition that affects approximately 1 in every 20,000 - 50,000 live births. WBS children have specific skeletal deformities, dental malformations and rare lingual muscle dysfunction. The need for orthodontic and orthognathic therapy has arisen and has been considered a real clinical challenge even for experienced professionals, once it requires a complex and individualized treatment plan. This study reports a case of orthopedic expansion of the maxilla, in which a modified facial mask was used for protraction of the maxillary complex associated with clockwise rotation of the maxilla. In addition, special considerations about treatment time and orthopedic outcomes are discussed.
Subject
Oral Surgery,Orthodontics
Reference32 articles.
1. Williams syndrome;Oncag A;J Clin Pediatr Dent,1995
2. Post-natal size and morphology of the sella turcica in Williams syndrome;Axelsson S;Eur J Orthod,2004
3. Deletions of the elastin gene at 7q11.23 occur in approximately 90% of patients with Williams syndrome;Nickerson E;Am J Hum Genet,1995
4. The role of dental evaluation and cephalometric analysis in the diagnosis of Williams-Beuren syndrome;Tarjan I;Wien Klin Wochenschr,2005
5. Prevalence estimation of Williams syndrome;Strømme P;J Child Neurol,2002
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