Neurological disorders associated with glutamic acid decarboxylase antibodies: a Brazilian series

Author:

Fernandes Maurício1,Munhoz Renato P.2,Carrilho Paulo Eduardo Mestrinelli3,Arruda Walter O.1,Lorenzoni Paulo J.1,Scola Rosana H.1,Werneck Lineu César1,Teive Hélio A. G.1

Affiliation:

1. Universidade Federal do Paraná, Brazil

2. Pontifícia Universidade Católica, Brazil

3. Universidade Estadual do Oeste do Paraná, Brazil

Abstract

Neurological disorders associated with glutamic acid decarboxylase (GAD) antibodies are rare pleomorphic diseases of uncertain cause, of which stiff-person syndrome (SPS) is the best-known. Here, we described nine consecutive cases of neurological disorders associated with anti-GAD, including nine patients with SPS and three cases with cerebellar ataxia. Additionally, four had hypothyroidism, three epilepsy, two diabetes mellitus and two axial myoclonus.

Publisher

FapUNIFESP (SciELO)

Subject

Neurology,Neurology (clinical)

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