Unilateral pulmonary agenesis, esophageal atresia, and tracheo esophageal fistula: no more a fatal condition

Abstract

The occurrence of unilateral pulmonary agenesis (PA) and esophageal atresia with and without tracheo esophageal fistula (EA/TEF) is exceedingly rare. The common origin of the esophagus and the lungs from the primordial foregut explains this association. This study reports on the accuracy of the preoperative investigations, operative approach, and a review of the literature and our own series.