Abstract
Inflammatory myofibroblastic tumor of the lung is a very rare tumor in childhood. We present the clinical case of an 11-year-old boy who came to the emergency room due to very mild hemoptysis that lasted a few hours, without other symptoms or signs associated. The rapid onset of hypovolemic shock forced us to perform an urgent thoracotomy. A large tumor with uncontrollable bleeding was found and a right pneumonectomy was performed.