Unilateral Nevus of Ota with Palatal and Optic Disc Pigmentation with Coincidental Preauricular Tag- A Case Report

Abstract

Nevus of Ota also known as oculodermal melanosis presents as hyperpigmentation of face involving ophthalmic and maxillary branches of trigeminal nerve associated with ocular hyperpigmentation. It is due to confinement of melanocytes in the dermis. Most commonly it is unilateral but sometimes it may have bilateral presentation. Typically, it presents at birth but can also be an acquired condition. Frequently seen in Japanese and rarely in Indian subcontinent. It has more predilection towards females. Less frequently, hyperpigmentation is seen in other sites like oral mucosa, tympanum and nasal mucosa. These patients are at high risk of developing glaucoma and malignancy. The author reported a case of 12-year-old male child with unilateral pigmentation of left side face involving forehead, periorbital and cheek, along with ocular pigmentation. Hyperpigmentation of conjunctiva, iris and angles is present in left eye with intraocular pressure being normal in both eyes. Fundus showing optic disc pigmentation in the left eye with cup disc asymmetry in both eyes. Child has coexistent preauricular tag on the left side.