Author:
Jamali Elena,Sharifi Guive,Ghafouri-Fard Soudeh,Bidari Zerehpoosh Farahnaz,Yazdanpanahi Mahmood,Taheri Mohammad
Abstract
IntroductionRosai-Dorfman disease (RDD) usually presents with painless cervical lymphadenopathy during the two first decades of life, with or without extranodal involvement. Exclusive extranodal manifestation, and especially central nervous system (CNS) involvement, is uncommon. The etiology remains unknown and definitive diagnosis is based on characteristic histopathological and immunohistochemical features showing S100(+) CD1a(−) RDD type histiocytes with emperipolesis. Most CNS cases are dural-based masses.Case PresentationHerein, we present a case of RDD in an 8-year-old boy, who presented with multiple huge intraventricular masses.ConclusionRegarding rare CNS involvement and lack of established evidence-based therapeutic approaches, reports of any individual case can supply further beneficial data concerning treatment approaches and long-term effectiveness of therapeutic strategies.
Cited by
4 articles.
订阅此论文施引文献
订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献