Management of Ebstein Anomaly in the Current Era: The Story of One Fetus and the Collaboration of Many

Management of Ebstein Anomaly in the Current Era: The Story of One Fetus and the Collaboration of Many—A Case Report

Published:2024-05-09 Issue:5 Volume:11 Page:147
ISSN:2308-3425
Container-title:Journal of Cardiovascular Development and Disease
language:en
Short-container-title:JCDD

Author:

Kavanaugh-McHugh Ann¹^ORCID,Zuckerwise Lisa C.²^ORCID,Killen Stacy A. S.¹,Morris Emily A.³^ORCID,Sullivan Rachel T.¹^ORCID,Alrifai Mhd Wael³^ORCID,Bichell David P.⁴,Smith-Parrish Melissa⁵^ORCID,Freud Lindsay⁶

Affiliation:

1. Thomas. P. Graham Jr. Division of Pediatric Cardiology, Department of Pediatrics, Monroe Carell Jr. Children’s Hospital at Vanderbilt, Vanderbilt University Medical Center, Nashville, TN 37232, USA

2. Division of Maternal-Fetal Medicine, Department of Obstetrics and Gynecology, University of Virginia School of Medicine, Charlottesville, VA 22908, USA

3. Division of Neonatology, Department of Pediatrics, Monroe Carell Jr. Children’s Hospital at Vanderbilt, Vanderbilt University Medical Center, Nashville, TN 37232, USA

4. Department of Cardiac Surgery, Vanderbilt University Medical Center, Nashville, TN 37232, USA

5. Division of Critical Care Medicine, Department of Pediatrics, Monroe Carell Jr. Children’s Hospital at Vanderbilt, Vanderbilt University Medical Center, Nashville, TN 37232, USA

6. Department of Paediatrics, The Hospital for Sick Children, University of Toronto, Toronto, ON M5G 1X8, Canada

Abstract

Collaborative multicenter research has significantly increased our understanding of fetal Ebstein anomaly, delineating risk factors for adverse outcomes as well as predictors of postnatal management. These data are incorporated into prenatal care and therapeutic strategies and inform family counseling and delivery planning to optimize care. This report details the translation of findings from multicenter studies into multidisciplinary prenatal care for a fetus with Ebstein anomaly, supraventricular tachycardia, and a circular shunt, including transplacental therapy to control arrhythmias and achieve ductal constriction, informed and coordinated delivery room management, and planned univentricular surgical palliation.

Publisher

MDPI AG

Link

https://www.mdpi.com/2308-3425/11/5/147/pdf

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