Recommendations for the Clinical Approach to Immune Thrombocytopenia: Spanish ITP Working Group (GEPTI)

Author:

Mingot-Castellano María1,Canaro Hirnyk Mariana2,Sánchez-González Blanca3,Álvarez-Román María4,Bárez-García Abelardo5ORCID,Bernardo-Gutiérrez Ángel6ORCID,Bernat-Pablo Silvia7,Bolaños-Calderón Estefanía8,Butta-Coll Nora9ORCID,Caballero-Navarro Gonzalo10,Caparrós-Miranda Isabel11,Entrena-Ureña Laura12,Fernández-Fuertes Luis13,García-Frade Luis14,Gómez del Castillo María15,González-López Tomás16ORCID,Grande-García Carlos17,Guinea de Castro José18ORCID,Jarque-Ramos Isidro19,Jiménez-Bárcenas Reyes20ORCID,López-Ansoar Elsa21,Martínez-Carballeira Daniel6ORCID,Martínez-Robles Violeta22,Monteagudo-Montesinos Emilio23,Páramo-Fernández José24ORCID,Perera-Álvarez María25,Soto-Ortega Inmaculada6,Valcárcel-Ferreiras David26,Pascual-Izquierdo Cristina2728

Affiliation:

1. Hematology Department, Hospital Universitario Virgen del Rocío, Instituto de Biomedicina de Sevilla, 41013 Sevilla, Spain

2. Hematology Department, Hospital Son Espases, Palma de Mallorca, 07210 Palma, Spain

3. Hematology Department, Hospital del Mar, 08003 Barcelona, Spain

4. Hematology Department, Hospital Universitario La Paz-IdiPAZ, Universidad Autónoma de Madrid, 28046 Madrid, Spain

5. Hematology Department, Hospital de Ávila, 05004 Ávila, Spain

6. Hematology Department, Hospital Central de Asturias, 33011 Oviedo, Spain

7. Hematology Department, Hospital Universitario de la Plana, 12540 Villarreal, Spain

8. Hematology Department, Hospital Clínico San Carlos, IML, IdISSC, 28040 Madrid, Spain

9. Hematology Department, Instituto de Investigación Hospital Universitario La Paz (IdiPAZ), 28046 Madrid, Spain

10. Hematology Department, Hospital Universitario Miguel Servet, 50009 Zaragoza, Spain

11. Hematology Department, Hospital Universitario Virgen de la Victoria, 29010 Málaga, Spain

12. Hematology Department, Hospital Universitario Virgen de las Nieves, 18014 Granada, Spain

13. Hematology Department, Complejo Hospitalario Universitario Insular Materno-Infantil, 35016 Las Palmas de Gran Canaria, Spain

14. Hematology Department, Hospital Universitario Río Hortega, Gerencia Regional de Salud de Castilla y León, 47012 Valladolid, Spain

15. Hematology Department, Hospital General de la Coruña, 15006 A Coruña, Spain

16. Hematology Department, Hospital Universitario de Burgos, 09006 Burgos, Spain

17. Hematology Department, Clínica Universidad de Navarra, 28022 Madrid, Spain

18. Hematology Department, Hospital Universitario de Araba, 01009 Vitoria-Gasteiz, Spain

19. Hematology Department, Hospital Universitario y Politécnico La Fe, 46026 Valencia, Spain

20. Hematology Department, Hospital Serranía de Ronda, 29400 Ronda, Spain

21. Hematology Department, Complejo Hospitalario Universitario de Vigo, 36312 Vigo, Spain

22. Hematology Department, Complejo Asistencial Universitario de León, 24008 León, Spain

23. Pediatric Department, Hospital Universitario y Politécnico La Fe, 46026 Valencia, Spain

24. Hematology Department, Clínica Universidad de Navarra, 31008 Pamplona, Spain

25. Hematology Department, Hospital Universitario de Gran Canaria Doctor Negrín, 35010 Las Palmas de Gran Canaria, Spain

26. Hematology Department, Vall d’Hebron Instituto de Oncología (VHIO), Universitat Autònoma de Barcelona, 08035 Barcelona, Spain

27. Hematology Department, Hospital General Universitario Gregorio Marañón (HGUGM) Madrid, Instituto de Investigación Gregorio Marañón, 28007 Madrid, Spain

28. Spanish Immune Thrombocytopenia Group, 28040 Madrid, Spain

Abstract

Primary immune thrombocytopenia (ITP) is a complex autoimmune disease whose hallmark is a deregulation of cellular and humoral immunity leading to increased destruction and reduced production of platelets. The heterogeneity of presentation and clinical course hampers personalized approaches for diagnosis and management. In 2021, the Spanish ITP Group (GEPTI) of the Spanish Society of Hematology and Hemotherapy (SEHH) updated a consensus document that had been launched in 2011. The updated guidelines have been the reference for the diagnosis and management of primary ITP in Spain ever since. Nevertheless, the emergence of new tools and strategies makes it advisable to review them again. For this reason, we have updated the main recommendations appropriately. Our aim is to provide a practical tool to facilitate the integral management of all aspects of primary ITP management.

Publisher

MDPI AG

Subject

General Medicine

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