Updated Review and Clinical Recommendations for the Diagnosis and Treatment of Patients with Retroperitoneal Sarcoma by the Spanish Sarcoma Research Group (GEIS)

Author:

Álvarez Álvarez Rosa1,Manzano Aránzazu2,Agra Pujol Carolina3ORCID,Artigas Raventós Vicente4,Correa Raquel5ORCID,Cruz Jurado Josefina6,Fernandez Juan Angel7,Garcia del Muro Xavier8,Gonzalez Jose Antonio4,Hindi Nadia91011,Lozano Lominchar Pablo12ORCID,Martínez-Trufero Javier13ORCID,Méndez Ramiro14ORCID,Muñoz Mercedes15,Muñoz Casares Cristobal16,Orbis Castellanos Francisco17,Orellana Fernandez Ruth18ORCID,Paniagua González Miguel19ORCID,Redondo Andres20ORCID,Valverde Morales Claudia21,Asencio Jose Manuel12ORCID

Affiliation:

1. Medical Oncology Department, Instituto de Investigacion Sanitaria Gregorio Marañon, Hospital Universitario Gregorio Marañon, 28007 Madrid, Spain

2. Medical Oncology Department, Hospital Universitario Clínico San Carlos, 28040 Madrid, Spain

3. Pathology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain

4. Surgery Department, Hospital Universitario Sant Pau, Universidad Autonoma de Barcelona, 08035 Barcelona, Spain

5. Radiation Oncology Department, Hospital Virgen de la Victoria, 29010 Malaga, Spain

6. Medical Oncology Department, Hospital Universitario Canarias, 38320 Santa Cruz de Tenerife, Spain

7. Sarcoma Multidisciplinary Unit, Surgery Department, Hospital Virgen de la Arrixaca, 30120 Murcia, Spain

8. Sarcoma Multidisciplinary Unit, Medical Oncology Department, Idibell, Instituto Catalan Oncología Hospitalet, 08908 Barcelona, Spain

9. Medical Oncology Department, Fundacion Jimenez Diaz University Hospital, 28040 Madrid, Spain

10. Medical Oncology Department, Hospital General de Villalba, 28400 Madrid, Spain

11. Health Research Institute-Fundación Jiménez Díaz (IIS-FJD), Universidad Autónoma de Madrid (UAM), 28040 Madrid, Spain

12. Surgery Department, Hospital Universitario Gregorio Marañon, Complutense University, 28040 Madrid, Spain

13. Medical Oncology Department, Hospital Universitario Miguel Servet, 50009 Zaragoza, Spain

14. Radiology Department, Hospital Universitario Clínico San Carlos, 28040 Madrid, Spain

15. Radiation Oncology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain

16. Surgery Department, Hospital San Juan de Dios, 14012 Cordoba, Spain

17. Sarcoma Multidisciplinary Unit, Surgery Department, Hospital Universitario y Politécnico La Fe, 46026 Valencia, Spain

18. Pathology Department, Hospital Universitario Santa Creu i Sant Pau, 08025 Barcelona, Spain

19. Radiology Department, Hospital Universitario Gregorio Marañon, Complutense University, 28007 Madrid, Spain

20. Medical Oncology Department, Hospital Universitario La Paz—IdiPAZ, 28046 Madrid, Spain

21. Medical Oncology Department, Vall D’Hebron University Hospital, 08035 Barcelona, Spain

Abstract

Soft tissue sarcomas (STS) are an uncommon and biologically heterogeneous group of tumors arising from mesenchymal cells. The incidence is estimated at five cases per 100,000 people per year. Retroperitoneal sarcomas (RPS) account for 10–15% of all STS, and their management depends on their anatomical characteristics and histotype. Due to their very low incidence, it is recommended that RPS be treated in reference centers and evaluated by an experienced multidisciplinary team (MDT). In Spain, the Spanish Group for Research in Sarcomas (GEIS) brings together experts from various specialties to promote research on sarcomas and improve treatment results. This paper summarizes the GEIS recommendations for the diagnosis, treatment, and follow-up of patients with RPS.

Publisher

MDPI AG

Subject

Cancer Research,Oncology

Reference106 articles.

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