Affiliation:
1. N.V. Sklifosovsky Research Institute for Emergency Medicine
Abstract
The article presents a clinical observation of an extremely rare in gynecological practice androgen insensitivity syndrome (AIS). The authors give data on the pathogenesis of the disease, modern classification and terminology of various forms of this pathology. The phenotypic manifestations of the disease, the results of clinical and instrumental studies and surgical treatment are described.The results of the study show the possibility of clinical diagnosis of AIS and timely surgical treatment of patients with this pathology, due to the high risk of gonadal malignancy.
Publisher
The Scientific and Practical Society of Emergency Medicine Physicians
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