Pigment variant of neuronal ceroid-lipofuscinosis
Author:
Publisher
Wiley
Subject
Genetics(clinical)
Reference17 articles.
1. KUFS' DISEASE: A CRITICAL REAPPRAISAL
2. Loss of pigment-laden stellate cells: A severe alteration of the isocortex in juvenile neuronal ceroid-lipofuscinosis
3. Pigmentoarchitectonic pathology of the isocortex in juvenile neuronal ceroid-lipofuscinosis: Axonal enlargements in layer IIIab and cell loss in layer V
4. Pigment Variant of Neuronal Ceroid-Lipofuscinosis (Kufs’ Disease)
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1. A Comparative Morphologic Analysis of Adult Onset Leukodystrophy With Neuroaxonal Spheroids and Pigmented Glia-A Role for Oxidative Damage;Journal of Neuropathology & Experimental Neurology;2007-07
2. Progression of early postnatal retinal pathology in a mouse model of neuronal ceroid lipofuscinosis;Eye;2004-11-26
3. Retinal Pathology and Function in a Cln3 Knockout Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis (Batten Disease);Molecular and Cellular Neuroscience;2002-04
4. 1 Neuronal ceroid lipofuscinoses: Classification and diagnosis;Batten Disease: Diagnosis, Treatment, and Research;2001
5. Neuronal ceroid lipofuscinoses: a review;The Italian Journal of Neurological Sciences;1998-10
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