Selective neurodegeneration in murine mucopolysaccharidosis VII is progressive and reversible
Author:
Publisher
Wiley
Subject
Clinical Neurology,Neurology
Reference47 articles.
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2. The mucopolysaccharidoses. In: eds. Metabolic basis of inherited disease. 8th ed. New York: McGraw-Hill, 2000: 3421-3452.
3. Beta glucuronidase deficiency: Report of clinical, radiologic, and biochemical features of a new mucopolysaccharidosis
4. Murine mucopolysaccharidosis type VII. Characterization of a mouse with beta-glucuronidase deficiency.
5. Neural progenitor cell engraftment corrects lysosomal storage throughout the MRS VII mouse brain
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