Elexacaftor/tezacaftor/ivacaftor in children aged 6–11 years with cystic fibrosis, at least one F508DEL allele, and advanced lung disease: A 24‐week observational study

Author:

Salvatore Donatello1ORCID,Cimino Giuseppe2,Troiani Patrizia2,Bignamini Elisabetta3,Esposito Irene3,Leonetti Giuseppina4,Zanda Maurizio5,Manunza Daniela5,Pepe Angela16

Affiliation:

1. Cystic Fibrosis Centre, Hospital San Carlo Potenza Italy

2. Lazio Reference Centre for Cystic Fibrosis Policlinico Umberto I University Hospital Rome Italy

3. Pediatric Pulmonology Unit, Città della Salute e della Scienza Ospedale Infantile Regina Margherita Turin Italy

4. Pediatric Cystic Fibrosis Centre Azienda Universitaria Ospedaliera Consorziale Policlinico Bari Italy

5. Cystic Fibrosis Center, Azienda Ospedaliera Brotzu Cagliari Italy

6. Department of Medicine, Surgery and Dentistry, Scuola Medica Salernitana, Postgraduate School of Pediatrics University of Salerno Baronissi Italy

Publisher

Wiley

Subject

Pulmonary and Respiratory Medicine,Pediatrics, Perinatology and Child Health

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