Cardiac tissue citric acid cycle intermediates in exercised very long‐chain acyl‐CoA dehydrogenase‐deficient mice fed triheptanoin or medium‐chain triglyceride-Reference-Cited by-同舟云学术

Cardiac tissue citric acid cycle intermediates in exercised very long‐chain acyl‐CoA dehydrogenase‐deficient mice fed triheptanoin or medium‐chain triglyceride

Published:2020-08-04 Issue:6 Volume:43 Page:1232-1242
ISSN:0141-8955
Container-title:Journal of Inherited Metabolic Disease
language:en
Short-container-title:Jrnl of Inher Metab Disea

Author:

Gaston Garen¹,Gangoiti Jon A.²,Winn Shelley¹,Chan Benjamin³,Barshop Bruce A.²,Harding Cary O.¹,Gillingham Melanie B.¹^ORCID

Affiliation:

1. Department of Molecular and Medical Genetics Oregon Health & Science University Portland Oregon USA

2. Department of Pediatrics, Genetics Division, Biochemical Genetics Program University of California San Diego La Jolla California USA

3. Biostatistics and Design Program, School of Public Health Oregon Health & Science University Portland Oregon USA

Publisher

Wiley

Subject

Genetics(clinical),Genetics

Link

https://onlinelibrary.wiley.com/doi/pdf/10.1002/jimd.12284

Reference33 articles.

1. Tricarboxylic acid cycle intermediate pool size and estimated cycle flux in human muscle during exercise

2. Pyruvate carboxylase deficiency: clinical and biochemical response to anaplerotic diet therapy

3. Dietary anaplerotic therapy improves peripheral tissue energy metabolism in patients with Huntington's disease

4. Treatment of cardiomyopathy and rhabdomyolysis in long-chain fat oxidation disorders using an anaplerotic odd-chain triglyceride

5. Carnitine palmitoyltransferase II deficiency: Successful anaplerotic diet therapy

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