Endoplasmic reticulum polymers impair luminal protein mobility and sensitize to cellular stress in alpha1‐antitrypsin deficiency-Reference-Cited by-同舟云学术

Endoplasmic reticulum polymers impair luminal protein mobility and sensitize to cellular stress in alpha1‐antitrypsin deficiency

Published:2013-03-14 Issue:5 Volume:57 Page:2049-2060
ISSN:0270-9139
Container-title:Hepatology
language:en
Short-container-title:Hepatology

Author:

Ordóñez Adriana¹,Snapp Erik L.²,Tan Lu¹,Miranda Elena¹³,Marciniak Stefan J.¹,Lomas David A.¹

Affiliation:

1. Department of Medicine, University of Cambridge, Cambridge Institute for Medical Research, Cambridge, UK

2. Department Anatomy and Structural Biology, Albert Einstein College of Medicine of Yeshiva University, Bronx, NY

3. Dipartimento di Biologia e Biotecnologie “Charles Darwin” e Istituto Pasteur–Fondazione Cenci Bolognetti, Università di Roma “La Sapienza,” Rome, Italy

Publisher

Wiley

Subject

Hepatology

Link

https://onlinelibrary.wiley.com/doi/pdf/10.1002/hep.26173

Reference31 articles.

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3. The mechanism of Z α1-antitrypsin accumulation in the liver

4. A novel monoclonal antibody to characterize pathogenic polymers in liver disease associated with α1-antitrypsin deficiency

5. Alpha 1‐antitrypsin Siiyama (Ser53‐‐>Phe). Further evidence for intracellular loop‐sheet polymerization;Lomas DA;J Biol Chem,1993

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