Desmoplastic small round cell tumors: Multimodality treatment and new risk factors

Author:

Scheer Monika1ORCID,Vokuhl Christian2,Blank Bernd1,Hallmen Erika1,von Kalle Thekla3,Münter Marc4,Wessalowski Rüdiger5,Hartwig Maite6,Sparber-Sauer Monika1ORCID,Schlegel Paul-Gerhardt7,Kramm Christof M.8,Kontny Udo9,Spriewald Bernd10,Kegel Thomas11,Bauer Sebastian12,Kazanowska Bernarda13,Niggli Felix14,Ladenstein Ruth15,Ljungman Gustaf16,Jahnukainen Kirsi17,Fuchs Jörg18,Bielack Stefan S.119,Klingebiel Thomas20,Koscielniak Ewa121,

Affiliation:

1. Pediatrics 5; Olgahospital; Klinikum Stuttgart Stuttgart Germany

2. Kiel Peadiatric Tumour Registry, Department of Pediatric Pathology; University Hospital Kiel; Germany

3. Radiologisches Institut; Olgahospital; Klinikum Stuttgart Stuttgart Germany

4. Radiation Oncology; Klinikum Stuttgart Stuttgart Germany

5. Pediatric Oncology Clinic; Heinrich-Heine-University Düsseldorf; Düsseldorf Germany

6. Pediatric Hematology and Oncology; University Hamburg-Eppendorf; Hamburg Germany

7. Children's Hospital, Pediatric Oncology; University Würzburg; Würzburg Germany

8. Pediatric Hematology and Oncology; University Medical Center Göttingen; Göttingen Germany

9. Pediatric Hematology and Oncology; University Medical Center Aachen; Aachen Germany

10. Internal Medicine 5; University Hospital Erlangen; Erlangen Germany

11. Hematology/Oncology; University of Halle; Halle Germany

12. Sarcoma Center, West German Cancer Center; University of Duisburg-Essen; Essen Germany

13. Department of Pediatric Hematology/Oncology and BMT; University of Wroclaw; Wroclaw Poland

14. Pediatric Oncology; University of Zürich; Zürich Switzerland

15. St. Anna Kinderspital and St. Anna Kinderkrebsforschung e.V.; Vienna Austria

16. Department of Women’s and Children’s Health; Uppsala University; Uppsala Sweden

17. Pediatrics; Helsinki University Central Hospital; Helsinki Finland

18. Pediatric Surgery; University Hospital Tübingen; Tübingen Germany

19. Pediatric Hematology and Oncology; University Children’s Hospital Münster; Münster Germany

20. Department for Children and Adolescents; University Hospital, Goethe-University Frankfurt (Main); Frankfurt Germany

21. Pediatric Hematology and Oncology; University of Tübingen; Tübingen Germany

Funder

Deutsche Kinderkrebsstiftung

Förderkreis Krebskranke Kinder e.V. Stuttgart

Deutsche Krebshilfe

Publisher

Wiley

Subject

Cancer Research,Radiology, Nuclear Medicine and imaging,Oncology

Reference65 articles.

1. Complete cytoreduction and HIPEC improves survival in desmoplastic small round cell tumor;Hayes-Jordan;Ann Surg Oncol,2014

2. Fusion of the EWS and WT1 genes in the desmoplastic small round cell tumor;Ladanyi;Cancer Res,1994

3. Case 2. Desmoplastic small cell tumor with divergent differentiation;Gerald;Pediatr Pathol,1989

4. Desmoplastic small round cell tumor: a nationwide study of a rare sarcoma;Stiles;J Surg Oncol,2018

5. Treatment for soft tissue sarcoma in childhood and adolescence. Austrian results within the CWS 96 study;Modritz;Wien Klin Wochenschr,2005

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