Osteoblast Malfunction Caused by Cell Stress Response to Procollagen Misfolding in α2(I)-G610C Mouse Model of Osteogenesis Imperfecta

Author:

Mirigian Lynn S12,Makareeva Elena1,Mertz Edward L1,Omari Shakib1,Roberts-Pilgrim Anna M1,Oestreich Arin K3,Phillips Charlotte L4,Leikin Sergey1

Affiliation:

1. Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD); National Institutes of Health; Bethesda MD USA

2. Department of Cell Biology; University of Texas Medical Branch; Galveston TX USA

3. Division of Biological Sciences; University of Missouri; Columbia MO USA

4. Department of Biochemistry; University of Missouri; Columbia MO USA

Funder

Intramural Research Program of NICHD

Publisher

Wiley

Subject

Orthopedics and Sports Medicine,Endocrinology, Diabetes and Metabolism

Reference38 articles.

1. Rosen CJ. 2013 1078

2. Chaperoning osteogenesis: new protein-folding disease paradigms;Makareeva;Trends Cell Biol,2011

3. Makareeva E Leikin S. Shapiro JR Byers PH Glorieux FH Sponseller PD 2014 71- 84

4. A molecular ensemble in the rER for procollagen maturation;Ishikawa;Biochim Biophys Acta,2013

5. Shapiro JR Byers PH Glorieux FH Sponseller PD. 2014 555

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