Probucol ameliorates renal and metabolic sequelae of primary CoQ deficiency inPdss2mutant mice

Author:

Falk Marni J.12,Polyak Erzsebet1,Zhang Zhe3,Peng Min4,King Rhonda5,Maltzman Jonathan S.5,Okwuego Ezinne1,Horyn Oksana2,Nakamaru‐Ogiso Eiko6,Ostrovsky Julian1,Xie Letian X.7,Chen Jia Yan7,Marbois Beth7,Nissim Itzhak26,Clarke Catherine F.7,Gasser David L.4

Affiliation:

1. Division of Human Genetics, Department of Pediatrics, The Children's Hospital of Philadelphia, Philadelphia, PA, USA

2. Division of Metabolic Disease, Department of Pediatrics, The Children's Hospital of Philadelphia, Philadelphia, PA, USA

3. Division of Biomedical Informatics, Department of Pediatrics, The Children's Hospital of Philadelphia, Philadelphia, PA, USA

4. Department of Genetics, University of Pennsylvania School of Medicine, Philadelphia, PA, USA

5. Department of Medicine, University of Pennsylvania School of Medicine, Philadelphia, PA, USA

6. Department of Biochemistry and Biophysics, University of Pennsylvania School of Medicine, Philadelphia, PA, USA

7. Department of Chemistry and Biochemistry, University of California Los Angeles, Los Angeles, CA, USA

Publisher

EMBO

Subject

Molecular Medicine

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