Characterization of two rat models of cystic fibrosis—KO and F508del CFTR—Generated by Crispr‐Cas9-Reference-Cited by-同舟云学术

Characterization of two rat models of cystic fibrosis—KO and F508del CFTR—Generated by Crispr‐Cas9

Published:2019-11-25 Issue:4 Volume:2 Page:297-311
ISSN:2576-2095
Container-title:Animal Models and Experimental Medicine
language:en
Short-container-title:Anim Models Exp Med

Author:

Dreano Elise¹,Bacchetta Marc²,Simonin Juliette²,Galmiche Louise³,Usal Claire⁴⁵,Slimani Lotfi⁶⁷^ORCID,Sadoine Jérémy⁶^ORCID,Tesson Laurent⁴⁵,Anegon Ignacio⁴⁵,Concordet Jean‐Paul⁸,Hatton Aurélie¹,Vignaud Lucile¹,Tondelier Danielle¹,Sermet‐Gaudelus Isabelle¹⁹¹⁰,Chanson Marc²^ORCID,Cottart Charles‐Henry¹⁹¹¹^ORCID

Affiliation:

1. INSERM 1151 INEM Université de Paris Paris France

2. Département de Pédiatrie Gynécologie & Obstétrique et Département de Physiologie Cellulaire & Métabolisme Université de Genève Genève Switzerland

3. Département de Pathologie APHP CHU Necker‐Enfants Malades Paris France

4. Centre de Recherche en Transplantation & Immunologie UMR 1064 INSERM Université de Nantes Nantes France

5. Plateforme Trangénèse Rat & ImmunoPhénomique INSERM 1064 & SFR François Bonamy CNRS UMS3556 Nantes France

6. Pathologie, Imagerie & Biothérapies Orofaciales Montrouge France

7. Plateforme Imageries du vivant Faculté de chirurgie dentaire Université de Paris Paris France

8. INSERM U1154 CNRS UMR7196 MNHN TACGENE Paris France

9. AP‐HP Centre Maladie Rare Mucoviscidose et Maladies du CFTR Assistance Publique Hôpitaux de Paris Hôpital Necker‐Enfants Malades Paris France

10. Faculté de Médecine de Paris Université de Paris Paris France

11. Faculté de Pharmacie de Paris Université de Paris Paris France

Funder

Association Vaincre la Mucoviscidose

Schweizerischer Nationalfonds zur Förderung der Wissenschaftlichen Forschung

Publisher

Wiley

Link

https://onlinelibrary.wiley.com/doi/pdf/10.1002/ame2.12091

Reference30 articles.

1. New animal models of cystic fibrosis: what are they teaching us?;Keiser NW;Curr Opin Pulm Med,2011

2. Cystic Fibrosis Mouse Models

3. Pathophysiology of Gene-Targeted Mouse Models for Cystic Fibrosis

4. Animal and model systems for studying cystic fibrosis

5. Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis

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