Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach

Author:

Menegueti Mayra Gonçalves1,Gil Cezar Alkmim-Teixeira1,Casarini Karin Aparecida1,Muniz Cordeiro Kátia Simone1,Basile-Filho Anibal1,Martins-Filho Olindo Assis2,Auxiliadora-Martins Maria1

Affiliation:

1. Divisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, Brazil

2. Laboratório de Biomarcadores de Diagnóstico e Monitoração, Instituto René Rachou, Fundação Oswaldo Cruz, Belo Horizonte, MG, Brazil

Abstract

Despite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential.

Publisher

Hindawi Limited

Subject

Critical Care and Intensive Care Medicine

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