Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature-Reference-Cited by-同舟云学术

Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature

Published:2013 Issue: Volume:2013 Page:1-6
ISSN:2090-6528
Container-title:Case Reports in Gastrointestinal Medicine
language:en
Short-container-title:Case Reports in Gastrointestinal Medicine

Author:

Samo Salih¹^ORCID,Sherid Muhammed²^ORCID,Husein Husein³^ORCID,Sulaiman Samian¹^ORCID,Yungbluth Margaret⁴,Vainder John A.¹

Affiliation:

1. Department of Internal Medicine, Division of Gastroenterology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USA

2. Department of Internal Medicine, Division of Gastroenterology, CGH Medical Center, 100 East LeFevre Road, Sterling, IL 61081, USA

3. Department of Internal Medicine, Division of Gastroenterology, University of Tishreen, Aleppo Street, P.O. Box 2230, Latakia, Syria

4. Department of Pathology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USA

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding. We report a case of a 32-year-old male with a known diagnosis of KTS who presented with a life-threatening rectal bleeding and was treated with proctosigmoidectomy and massive blood products transfusion. He expired after a long hospitalization. We then review the literature on KTS and management of some of its complications.

Publisher

Hindawi Limited

Subject

General Engineering

Link

http://downloads.hindawi.com/journals/crigm/2013/813653.pdf

Reference35 articles.

1. Pulmonary Thromboembolism Associated With Klippel-Trenaunay Syndrome

2. Klippel-Trénaunay Syndrome: Spectrum and Management

3. Evaluation and Management of Pain in Patients with Klippel-Trenaunay Syndrome: A Review

4. Klippel-Trenaunay syndrome with gastrointestinal bleeding, splenic hemangiomas and left inferior vena cava

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