Right Ventricular Outflow Tract Tachycardia with Structural Abnormalities of the Right Ventricle and Left Ventricular Diverticulum

Author:

Martini Bortolo1,Trevisi Nicola2,Martini Nicolò13,Zhang Li456

Affiliation:

1. Cardiovascular Unit, Alto Vicentino Hospital, Via Gioberti 9, 36016 Thiene, Italy

2. San Raffaele Hospital, 20132 Milan, Italy

3. Medical College, Ferrara Medical University, 44121 Ferrara, Italy

4. Lankenau Medical Center, Wynnewood, PA 19096, USA

5. Lankenau Institute for Medical Research, Wynnewood, PA 19096, USA

6. Jefferson Medical College, Thomas Jefferson University, Philadelphia, PA 19107, USA

Abstract

A 43-year-old woman presented to the emergency room with a sustained ventricular tachycardia (VT). ECG showed a QRS in left bundle branch block morphology with inferior axis. Echocardiography, ventricular angiography, and cardiac magnetic resonance imaging (CMRI) revealed a normal right ventricle and a left ventricular diverticulum. Electrophysiology studies with epicardial voltage mapping identified a large fibrotic area in the inferolateral layer of the right ventricular wall and a small area of fibrotic tissue at the anterior right ventricular outflow tract. VT ablation was successfully performed with combined epicardial and endocardial approaches.

Publisher

Hindawi Limited

Subject

Cardiology and Cardiovascular Medicine

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