The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses-Reference-Cited by-同舟云学术

The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses

Published:2017 Issue: Volume:2017 Page:1-5
ISSN:2090-6803
Container-title:Case Reports in Pediatrics
language:en
Short-container-title:Case Reports in Pediatrics

Author:

Congedi Sabrina¹^ORCID,Di Pede Chiara¹²^ORCID,Scarpa Maurizio¹³,Rampazzo Angelica¹,Benini Franca¹²

Affiliation:

1. Pediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, Italy

2. Pediatric Pain and Palliative Care Service, Padova, Italy

3. Laboratory of Diagnosis and Therapy of Lysosomal Disorders, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, Italy

Abstract

Mucopolysaccharidoses (MPSs) are a group of rare, genetic lysosomal storage disorders. They are caused by deficiencies of the lysosomal enzymes involved in the degradation of glycosaminoglycans (GAGs). Pain is a common feature in mucopolysaccharidoses. However, the pathophysiology of pain in this group of diseases is still unclear and genesis of pain is multifactorial. Currently, poor data about pain management in these patients are available. Here, we present our clinical experience in complex pain management in three children with MPS.

Publisher

Hindawi Limited

Subject

General Medicine

Link

http://downloads.hindawi.com/journals/cripe/2017/7257230.pdf

Reference23 articles.

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3. Mucopolysaccharidoses in the Scandinavian countries: incidence and prevalence

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