Erythema elevatum diutinum - Case report of a rare entity

Abstract

Erythema elevatum diutinum (EED) is a rare entity of chronic cutaneous vasculitis occurring in association with a variety of conditions including autoimmunity, infectious disease, and hematological abnormalities. The exact pathogenesis of EED is unknown. A 59-year old female presented with multiple, itchy, eczematized erythematous papules and plaques over both upper and lower limbs present since 5 months. Histopathological changes were consistent with EED. Patient was started on oral Dapsone 100mg bid along with topical betamethasone diproprionate cream. Within 6 weeks lesions regressed completely leaving post-inflammatory hyperpigmentation. Dapsone was stopped at the end of 3 months. Minor recurrences are managed by topical steroids. EED is a rare form of vasculitis which is difficult to diagnose clinically, histopathology can be diagnostic. Dapsone is the treatment of choice.