Rare cases of (SMMCI) solitary median maxillary central incisor syndrome: Identification and management

Abstract

Condition where there is agenesis of central maxillary incisor is unique and very rare with association of peculiar stomatognathic features is called (SMMCI) Solitary median maxillary central incisor syndrome which may or may not have systemic involvement, and the condition is found to affect 1:50,000 live births. SMMCI is a very rare abnormality in developing stage of fetus involving the tooth germs of central incisor. The most common systemic association is with holoprosencephaly, and diagnosis in early stage is of utmost importance for managing dental aesthetic issue patient generally suffers from the syndrome. The objective of current article is to discuss two cases of SMMCI syndrome; one with systemic involvement having esophageal Artesia, a rare entity with SMMCI syndrome and the other one without systemic involvement. In both cases, patient’s parents were not aware of the dental anomaly the child was suffering, and parents were highlighted on treatment options in managing such dental cases. As there are a significant number of SMMCI syndrome cases with systemic involvement and other developmental problems, it becomes prudent to have a quick and prompt diagnosis in initial stages of life and simultaneously the management approach becomes multidisciplinary.