Affiliation:
1. Kerala University of Health Sciences, Government Dental College Alappuzha, Vandanam, Kerala, India
2. Government Dental College Alappuzha, Vandanam, Kerala, India
Abstract
Neurofibromatosis type 1 (NF1), also known as von Recklinghausen disease, is an autosomal disease caused by mutations in the NF1 tumor suppressor gene. NF1 affects bones, nerves, soft tissues and skin. Oral manifestations of NF1 consist of soft tissue tumors, bone defects, periodontal and dental changes, and altered salivary flow. We report one such case, a 26-year-old man with Gingival enlargement, Café au lait spots, axillary freckling, and multiple nodules on his body.
Publisher
IP Innovative Publication Pvt Ltd
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