Anaesthetic considerations in paediatric klippel feil syndrome- A case report

Abstract

Klippel feil syndrome is a rare skeletal disorder primarily characterized by abnormal union or fusion of two or more cervical vertebrae which is often associated with cervical canal stenosis. This results in a short neck, a low hairline at the back of the head, a limited range of motion in the neck and infrequently an atlanto- axial instability. Here we report a case of type 3 paediatric Klippel Feil syndrome who underwent Sprengel deformity repair in prone position and its anesthetic implications.A careful assessment of airway and an algorithmic approach towards management is needed in children with KFS. The various spine deformities associated with KFS demand careful positioning and a reconfirmation of appropriate ETT position, airway pressures and lung compliance is recommended in these children.