Time Course of Pathogenic and Adaptation Mechanisms in Cystinotic Mouse Kidneys-Reference-Cited by-同舟云学术

Time Course of Pathogenic and Adaptation Mechanisms in Cystinotic Mouse Kidneys

Published:2014-02-13 Issue:6 Volume:25 Page:1256-1269
ISSN:1046-6673
Container-title:Journal of the American Society of Nephrology
language:en
Short-container-title:JASN

Author:

Gaide Chevronnay Héloïse P.,Janssens Virginie,Van Der Smissen Patrick,N’Kuli Francisca,Nevo Nathalie,Guiot Yves,Levtchenko Elena,Marbaix Etienne,Pierreux Christophe E.,Cherqui Stéphanie,Antignac Corinne,Courtoy Pierre J.

Publisher

American Society of Nephrology (ASN)

Subject

Nephrology,General Medicine

Reference50 articles.

1. Cystinosis

2. Cystinosis: the evolution of a treatable disease

3. Cystinosin, the protein defective in cystinosis, is a H+-driven lysosomal cystine transporter

4. Molecular pathogenesis of cystinosis: effect of CTNS mutations on the transport activity and subcellular localization of cystinosin

5. Renal phenotype of the cystinosis mouse model is dependent upon genetic background

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