Affiliation:
1. Pirogov Russian National Research Medical University
2. Pirogov Russian National Research Medical University; Filatov Children’s City Clinical Hospital
Abstract
Introduction. Congenital bronchopulmonary vascular malformations manifest a wide range of disorders in the three main components of the lungs: respiratory tract and lung parenchyma, arteries and veins. Malformations of all the main components of lung tissues, namely, arterial blood supply, venous outflow and respiratory tract - may be variants of a single primary complex of pulmonaryvascular anomalies.Observation. A described clinical case demonstrates an extremely interesting mixed bronchoarteriovenous malformation affecting the pulmonary respiratory tract, pulmonary artery and pulmonary vein. Various instrumental techniques were used for the diagnostics, the key of which was computed tomography with intravenous contrast.Conclusion. The article presents a wide range of pathological changes observed in this clinical case; it also analyzes the nature of each component and terminology.
Publisher
Union of the Medical Community "National Medical Chamber"
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