Quadricuspid Aortic Valve: Imaging, Diagnosis, and Prognosis

Author:

Alomari Mohammad1,El-Sayed Ahmed Magdy M.12,Ali Mostafa1,Wadiwala Ishaq J.1,Pham Si M.1,Sareyyupoglu Basar1

Affiliation:

1. 1Department of Cardiothoracic Surgery, Mayo Clinic, Jacksonville, Florida

2. 2Department of Surgery, Zagazig University Faculty of Medicine, Zagazig, Egypt

Abstract

Abstract Quadricuspid aortic valve is a rare congenital cardiac anomaly with an incidence of 0.008% to 0.043%. Its clinical course varies depending on cusp anatomy, function, and associated cardiac malformations. It frequently progresses to aortic valve regurgitation that may require surgical valve replacement. Detection has shifted from incidental discovery during autopsies or cardiac surgeries in the early 20th century to various cardiac imaging methods in recent decades. In addition to contributing to the literature, this report supports the use of transesophageal echocardiography more liberally to detect aortic valve abnormalities. The case presents a 48-year-old female patient with an incidentally discovered quadricuspid aortic valve.

Publisher

Texas Heart Institute Journal

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