Affiliation:
1. Veltischev Research and Clinical Institute for Pediatrics and Pediatric Surgery of the Pirogov Russian National Research Medical University
Abstract
We present a severe disease progression observed in a 13-year-old patient diagnosed with Marfan syndrome and associated cardiac rhythm disorders, including polymorphic ventricular premature contractions and persistent ventricular tachycardia resistant to a wide range of antiarrhythmic medications. We conducted an analysis of contemporary perspectives on the etiology of ventricular tachyarrhythmias and their impact on the prognosis of patients with Marfan syndrome. Conclusions were drawn regarding the selection of treatment strategies for this specific patient population.
Publisher
Institute of Cardio Technics - INCART
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