2-Methylcitric acid impairs glutamate metabolism and induces permeability transition in brain mitochondria

Author:

Amaral Alexandre Umpierrez1,Cecatto Cristiane1,Castilho Roger Frigério2,Wajner Moacir13

Affiliation:

1. Departamento de Bioquímica; Instituto de Ciências Básicas da Saúde; Universidade Federal de Rio Grande do Sul; Porto Alegre RS Brazil

2. Departamento de Patologia Clínica; Faculdade de Ciências Médicas; Universidade Estadual de Campinas; Campinas SP Brazil

3. Serviço de Genética Médica; Hospital de Clínicas de Porto Alegre; Porto Alegre RS Brazil

Funder

Conselho Nacional de Desenvolvimento Científico e Tecnológico

Fundação de Amparo à Pesquisa do Estado do Rio Grande do Sul

Fundação de Amparo à Pesquisa do Estado de São Paulo

PROPESQ/UFRGS

FINEP/IBN-Net

Instituto Nacional de Ciência e Tecnologia para Excitotoxicidade e Neuroproteção

Publisher

Wiley

Subject

Cellular and Molecular Neuroscience,Biochemistry

Reference75 articles.

1. Safranine as a probe of the mitochondrial membrane potential;Akerman;FEBS Lett.,1976

2. Evidence for catabolic pathway of propionate metabolism in CNS: expression pattern of methylmalonyl-CoA mutase and propionyl-CoA carboxylase alpha-subunit in developing and adult rat brain;Ballhausen;Neuroscience,2009

3. Properties of the permeability transition pore in mitochondria devoid of Cyclophilin D;Basso;J. Biol. Chem.,2005

4. Methylmalonic and propionic acidaemias: management and outcome;Baulny;J. Inherit. Metab. Dis.,2005

5. Modulation of the mitochondrial cyclosporin A-sensitive permeability transition pore by the proton electrochemical gradient. Evidence that the pore can be opened by membrane depolarization;Bernardi;J. Biol. Chem.,1992

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