Impaired Phosphorylation of Lysosomal Enzymes in Fibroblasts of Patients with Mucolipidosis III
Author:
Publisher
Wiley
Subject
Biochemistry
Link
http://onlinelibrary.wiley.com/wol1/doi/10.1111/j.1432-1033.1982.tb05856.x/fullpdf
Reference18 articles.
1. A hypothesis for I-cell disease: Defective hydrolases that do not enter lysosomes
2. Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts.
3. Enzymatic identification of mannose 6-phosphate on the recognition marker for receptor-mediated pinocytosis of beta-glucuronidase by human fibroblasts.
4. Identification of mannose 6-phosphate in glycoproteins that inhibit the assimilation of -galactosidase by fibroblasts
5. Biosynthesis of lysosomal enzymes in fibroblasts. Phosphorylation of mannose residues.
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