Canakinumab efficacy in refractory adult-onset PFAPA syndrome

Author:

Lopalco Giuseppe1,Rigante Donato2,Vitale Antonio3,Caso Francesco3,Iannone Florenzo1ORCID,Cantarini Luca3

Affiliation:

1. Rheumatology Unit; Interdisciplinary Department of Medicine; Policlinico of Bari; Bari Italy

2. Institute of Pediatrics; Università Cattolica Sacro Cuore; Fondazione Policlinico Universitario A. Gemelli; Rome Italy

3. Rheumatology Unit; Research Center of Systemic Autoinflammatory Diseases, and Behcet's Disease; Policlinico “Le Scotte”; University of Siena; Siena Italy

Publisher

Wiley

Subject

Rheumatology

Reference12 articles.

1. Syndrome of periodic fever, pharyngitis, and aphthous stomatitis;Marshall;J Pediatr,1987

2. Cytokine profile in PFAPA syndrome suggests continuous inflammation and reduced anti-inflammatory response;Stojanov;Eur Cytokine Netw,2006

3. Periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) is a disorder of innate immunity and Th1 activation responsive to IL-1 blockade;Stojanov;Proc Natl Acad Sci USA,2011

4. Periodic fever accompanied by aphthous stomatitis, pharyngitis and cervical adenitis syndrome (PFAPA syndrome) in adults;Padeh;Isr Med Assoc J,2008

5. Diagnosis of PFAPA syndrome applied to a cohort of 17 adults with unexplained recurrent fevers;Cantarini;Clin Exp Rheumatol,2012

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