Oxidative stress and mitochondrial dynamics malfunction are linked in P elizaeus‐ M erzbacher disease

Author:

Ruiz Montserrat12,Bégou Mélina34,Launay Nathalie12,Ranea‐Robles Pablo12ORCID,Bianchi Patrizia12,López‐Erauskin Jone12,Morató Laia12,Guilera Cristina12,Petit Bérengère5,Vaurs‐Barriere Catherine5,Guéret‐Gonthier Céline5,Bonnet‐Dupeyron Marie‐Noëlle6,Fourcade Stéphane12ORCID,Auwerx Johan7,Boespflug‐Tanguy Odile89,Pujol Aurora121011

Affiliation:

1. Neurometabolic Diseases Laboratory Bellvitge Biomedical Research Institute (IDIBELL), 08908 L'Hospitalet de Llobregat Barcelona Spain

2. Center for Biomedical Research on Rare Diseases (CIBERER), ISCIII Spain

3. Inserm, UMR 1107, NEURO‐DOL F‐63001 Clermont‐Ferrand France

4. Université Clermont Auvergne, NEURO‐DOL, BP 10448 F‐63000 Clermont‐Ferrand France

5. Université Clermont Auvergne, GReD, BP 10448 F‐63000 Clermont‐Ferrand France

6. CHU de Clermont Ferrand, Laboratoire de cytogénétique F‐63000 Clermont‐Ferrand France

7. Laboratory for Integrative and Systems Physiology École Polytechnique Fédérale de Lausanne, Station 15 CH‐1015 Lausanne Switzerland

8. Assistance Publique des Hopitaux de Paris (APHP), Reference Center for Rare Diseases “Leukodystrophies,” Child Neurology and Metabolic Disorders Department Robert Debré University Hospital Paris France

9. Inserm, Paris Diderot University UMR 1141, DHU PROTECT, Sorbonne Paris‐Cite Robert Debré University Hospital Paris France

10. Institute of Neuropathology University of Barcelona, L'Hospitalet de Llobregat Barcelona Spain

11. Catalan Institution of Research and Advanced Studies (ICREA) Barcelona Spain

Funder

European Commission

Instituto de Salud Carlos III

European Regional Development Fund

Conseil Régional d'Auvergne

Publisher

Wiley

Subject

Neurology (clinical),Pathology and Forensic Medicine,General Neuroscience

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