Successful treatment with 4‐phenylbutyrate in a patient with benign recurrent intrahepatic cholestasis type 2 refractory to biliary drainage and bilirubin absorption

Author:

Hayashi Hisamitsu1,Naoi Sotaro1,Hirose Yu1,Matsuzaka Yusuke1,Tanikawa Ken2,Igarashi Koji3,Nagasaka Hironori4,Kage Masayoshi2,Inui Ayano5,Kusuhara Hiroyuki1

Affiliation:

1. Laboratory of Molecular Pharmacokinetics, Graduate School of Pharmaceutical SciencesThe University of Tokyo Tokyo Japan

2. Department of Diagnostic PathologyKurume University Hospital Kurume Japan

3. Bioscience Division, Reagent Development DepartmentTOSOH Ayase Japan

4. Department of PediatricsTakarazuka City Hospital Takarazuka Japan

5. Department of Pediatric Hepatology and GastroenterologySaiseikai Yokohamashi Tobu Hospital Yokohama Japan

Funder

Astellas Foundation for Research on Metabolic Disorders

Grant-in-Aid for Scientific Research (C)

The Department of Research Promotion from Japan Agency for Medical Research and Development, AMED

Publisher

Wiley

Subject

Infectious Diseases,Hepatology

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