Liver histology of an afibrinogenemic patient with the Bβ-L353R mutation showing no evidence of hepatic endoplasmic reticulum storage disease (ERSD); comparative study in COS-1 cells of the intracellular processing of the Bβ-L353R fibrinogen vs. the ERSD-
Author:
Publisher
Wiley
Subject
Hematology
Link
http://onlinelibrary.wiley.com/wol1/doi/10.1111/j.1538-7836.2005.01229.x/fullpdf
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5. Fibrinogen biosynthesis. Assembly, intracellular degradation, and association with lipid synthesis and secretion;Redman;Ann N Y Acad Sci,2001
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