Improvement of medical care in a cohort of newborns with sickle-cell disease in North Paris: impact of national guidelines

Author:

Couque Nathalie1,Girard Delphine23,Ducrocq Rolande1,Boizeau Priscilla2ORCID,Haouari Zinedine45,Missud Florence45,Holvoet Laurent45,Ithier Ghislaine45,Belloy Marie6,Odièvre Marie-Héléne7,Benemou Michel8,Benhaim Patricia9,Retali Brigitte10,Bensaid Philippe11,Monier Brigitte12,Brousse Valentine13,Amira Roger14,Orzechowski Christine15,Lesprit Emmanuelle16,Mangyanda Laurent17,Garrec Nathalie18,Elion Jacques1319,Alberti Corinne2320,Baruchel André3421,Benkerrou Malika4520

Affiliation:

1. Génétique Moléculaire et Biochimie; AP-HP; Hôpital Robert-Debré; Paris France

2. Unité d'Epidémiologie Clinique; AP-HP; Hôpital Robert-Debré; Paris France

3. Univ Paris Diderot; Sorbonne Paris Cité; Paris France

4. Service d'Hématologie Pédiatrique; AP-HP; Hôpital Robert-Debré; Paris France

5. Centre de Référence de la Drépanocytose; Paris France

6. Hôpital Robert Ballanger; Aulnay sous Bois France

7. AP-HP; Hôpital Louis Mourier; Colombes France

8. Hôpital de Gonesse; Gonesse France

9. AP-HP; Hôpital Jean Verdier; Bondy France

10. Centre Hospitalier René Dubos; Pontoise France

11. Centre Hospitalier Victor Dupouy; Argenteuil France

12. Hôpital Simone Veil; Montmorency France

13. AP-HP; Hôpital Necker-Enfants Malades; Paris France

14. Centre Hospitalier Intercommunal de Saint-Denis; Saint-Denis France

15. Centre Hospitalier de Bry-sur-Marne; Bry-sur-Marne France

16. AP-HP; Hôpital Armand Trousseau; Paris France

17. CHI des Portes de l'Oise; Beaumont-sur-Oise France

18. Centre Hospitalier de Marne-la-Vallée; Jossigny France

19. Inserm UMR S1134; Paris France

20. Inserm 1123; Paris France

21. Institut Universitaire d'Hématologie (EA3518); Université Paris Diderot; Paris France

Funder

French Parisian Newborn Screening Organization

LVMH

Publisher

Wiley

Subject

Hematology

Reference42 articles.

1. Effectiveness of the 7-valent pneumococcal conjugate vaccine in children with sickle cell disease in the first decade of life;Adamkiewicz;Pediatrics,2008

2. Transcranial Doppler correlation with cerebral angiography in sickle cell disease;Adams;Stroke,1992

3. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography;Adams;New England Journal of Medicine,1998

4. AFDPHE 2013 Bilan d'activité de l'Association Française de Dépistage et de Prévention des Handicaps de l'Enfant http://www.afdphe.org/sites/default/files/bilan_activite_2013.pdf

5. Neonatal screening for haemoglobinopathies: the results of a 10-year programme in an English Health Region;Almeida;British Journal of Haematology,2001

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