Affiliation:
1. Evidence Based Child Health Unit Royal Liverpool Children's NHS Trust Alder Hey Liverpool UK
2. Institute of Child Health Royal Liverpool Children's NHS Trust Alder Hey Liverpool UK
Abstract
SUMMARYCystic fibrosis (CF) is one of the commonest lethal inherited conditions among Caucasians. It affects multiple organ systems and exhibits a range of clinical problems of varying severity. Life expectancy has improved in recent years as treatment regimes have become more intensive, but current treatments are expensive, often time consuming and may affect quality of life. This review summarises the treatments currently used in the management of patients with CF, and the evidence for these. (Int J Clin Pract 2000; 54(3): 171‐179)