Thoracic Society of Australia and New Zealand (TSANZ) position statement on chronic suppurative lung disease and bronchiectasis in children, adolescents and adults in Australia and New Zealand

Author:

Chang Anne B.123ORCID,Bell Scott C.456ORCID,Byrnes Catherine A.78,Dawkins Paul910,Holland Anne E.111213ORCID,Kennedy Emma141516,King Paul T.17ORCID,Laird Pamela181920ORCID,Mooney Sarah921,Morgan Lucy22,Parsons Marianne23,Poot Betty2425,Toombs Maree26,Torzillo Paul J.2728,Grimwood Keith2930

Affiliation:

1. Australian Centre for Health Services Innovation Queensland University of Technology Brisbane Queensland Australia

2. Department of Respiratory & Sleep Medicine Queensland Children's Hospital Brisbane Queensland Australia

3. NHMRC Centre for Research Excellence in Paediatric Bronchiectasis (AusBREATHE), Child Health Division, Menzies School of Health Research Charles Darwin University Darwin Northern Territory Australia

4. Thoracic Medicine The Prince Charles Hospital Brisbane Queensland Australia

5. Faculty of Medicine University of Queensland Brisbane Queensland Australia

6. Translational Research Institute Brisbane Queensland Australia

7. Department of Paediatrics University of Auckland Auckland New Zealand

8. Starship Children's Hospital Auckland New Zealand

9. Department of Respiratory Medicine Middlemore Hospital Auckland New Zealand

10. University of Auckland Auckland New Zealand

11. Department of Physiotherapy Alfred Health Melbourne Victoria Australia

12. Central Clinical School Monash University Melbourne Victoria Australia

13. Institute for Breathing and Sleep Heidelberg Victoria Australia

14. College of Medicine and Public Health Flinders University Darwin Northern Territory Australia

15. Board of Northern Territory General Practice Education Ltd Darwin Northern Territory Australia

16. Pandanus Medical NT Millner Northern Territory Australia

17. Departments of Respiratory and Sleep Medicine and Medicine, Monash Medical Centre Monash University Melbourne Victoria Australia

18. Department Physiotherapy Perth Children's Hospital Perth Western Australia Australia

19. Wal‐yan Respiratory Research Centre Telethon Kids Institute Perth Western Australia Australia

20. Department of Paediatrics, School of Medicine University of WA Perth Western Australia Australia

21. School of Clinical Sciences AUT University Auckland New Zealand

22. Department of Respiratory Medicine at Concord and Nepean Hospitals School of Medicine, Faculty of Medicine and Health, University of Sydney Sydney New South Wales Australia

23. Representative of Parent Advisory Group, NHMRC Centre of Research Excellence in Paediatric Bronchiectasis, Cough and Airways Research Group, Australian Centre for Health Services Innovation Queensland University of Technology Brisbane Queensland Australia

24. Respiratory Department Hutt Hospital, Te Whatu Ora Capital, Coast and Hutt Valley Lower Hutt New Zealand

25. School of Nursing Midwifery, and Health Practice Victoria University of Wellington Wellington New Zealand

26. School of Public Health University of Sydney Sydney New South Wales Australia

27. Nganampa Health Council Alice Springs Northwest Territories Australia

28. Royal Prince Alfred Hospital University of Sydney Sydney New South Wales Australia

29. School of Medicine and Dentistry, Menzies Health Institute Queensland Griffith University Southport Queensland Australia

30. Departments of Infectious Diseases and Paediatrics Gold Coast Health Southport Queensland Australia

Abstract

AbstractThis position statement, updated from the 2015 guidelines for managing Australian and New Zealand children/adolescents and adults with chronic suppurative lung disease (CSLD) and bronchiectasis, resulted from systematic literature searches by a multi‐disciplinary team that included consumers. The main statements are: Diagnose CSLD and bronchiectasis early; this requires awareness of bronchiectasis symptoms and its co‐existence with other respiratory diseases (e.g., asthma, chronic obstructive pulmonary disease). Confirm bronchiectasis with a chest computed‐tomography scan, using age‐appropriate protocols and criteria in children. Undertake a baseline panel of investigations. Assess baseline severity, and health impact, and develop individualized management plans that include a multi‐disciplinary approach and coordinated care between healthcare providers. Employ intensive treatment to improve symptom control, reduce exacerbation frequency, preserve lung function, optimize quality‐of‐life and enhance survival. In children, treatment also aims to optimize lung growth and, when possible, reverse bronchiectasis. Individualize airway clearance techniques (ACTs) taught by respiratory physiotherapists, encourage regular exercise, optimize nutrition, avoid air pollutants and administer vaccines following national schedules. Treat exacerbations with 14‐day antibiotic courses based upon lower airway culture results, local antibiotic susceptibility patterns, clinical severity and patient tolerance. Patients with severe exacerbations and/or not responding to outpatient therapy are hospitalized for further treatments, including intravenous antibiotics and intensive ACTs. Eradicate Pseudomonas aeruginosa when newly detected in lower airway cultures. Individualize therapy for long‐term antibiotics, inhaled corticosteroids, bronchodilators and mucoactive agents. Ensure ongoing care with 6‐monthly monitoring for complications and co‐morbidities. Undertake optimal care of under‐served peoples, and despite its challenges, delivering best‐practice treatment remains the overriding aim.

Funder

National Health and Medical Research Council

Publisher

Wiley

Subject

Pulmonary and Respiratory Medicine

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