Widespread alterations in the peripheral blood innate immune cell profile in cystic fibrosis reflect lung pathology
Author:
Affiliation:
1. School of Medicine University of Tasmania Hobart TAS Australia
2. Royal Hobart Hospital Hobart TAS Australia
3. Centenary Institute Newtown NSW Australia
4. Discipline of Pathology University of Sydney Sydney NSW Australia
Funder
University of Tasmania
Royal Hobart Hospital Research Foundation
Publisher
Wiley
Subject
Cell Biology,Immunology,Immunology and Allergy
Link
https://onlinelibrary.wiley.com/doi/pdf/10.1111/imcb.12230
Reference49 articles.
1. High Peripheral Blood Th17 Percent Associated with Poor Lung Function in Cystic Fibrosis
2. Intrinsic predisposition of naïve cystic fibrosis T cells to differentiate towards a Th17 phenotype
3. The immune response to chronic Pseudomonas aeruginosa lung infection in cystic fibrosis patients is predominantly of the Th2 typeNote
4. Reduced IL-10 secretion by CD4+ T lymphocytes expressing mutant cystic fibrosis transmembrane conductance regulator (CFTR)
5. Cytokine dysregulation in activated cystic fibrosis (CF) peripheral lymphocytes
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