Brain iron accumulation in Wilson disease: apost mortem7 Tesla MRI - histopathological study

Author:

Dusek P.12,Bahn E.3,Litwin T.4,Jabłonka-Salach K.5,Łuciuk A.5,Huelnhagen T.6,Madai V. I.7,Dieringer M. A.68,Bulska E.5,Knauth M.1,Niendorf T.68,Sobesky J.78,Paul F.89,Schneider S. A.1011,Czlonkowska A.412,Brück W.3,Wegner C.3,Wuerfel J.1913

Affiliation:

1. Institute of Neuroradiology; University Medical Center Göttingen; Göttingen Germany

2. Department of Neurology and Center of Clinical Neuroscience; 1 Faculty of Medicine and General University Hospital in Prague; Charles University in Prague; Praha Czech Republic

3. Institute of Neuropathology; University Medical Center Göttingen; Göttingen Germany

4. 2 Department of Neurology; Institute Psychiatry and Neurology; Warsaw Poland

5. Faculty of Chemistry; Biological and Chemical Research Centre; University of Warsaw; Warsaw Poland

6. Berlin Ultrahigh Field Facility (B.U.F.F.); Max-Delbrück Center for Molecular Medicine in the Helmholtz Association; Berlin Germany

7. Department of Neurology and Center for Stroke Research Berlin (CSB); Charité-Universitätsmedizin; Berlin Germany

8. Experimental and Clinical Research Center (ECRC); Charité-Universitätsmedizin and Max Delbrück Center for Molecular Medicine (MDC); Berlin Germany

9. NeuroCure Clinical Research Center and Clinical and Experimental Multiple Sclerosis Research Center; Department of Neurology; Charité-Universitätsmedizin; Berlin Germany

10. Neurology Department; University of Kiel; Kiel Germany

11. Department of Neurology; Ludwig-Maximilians-University; Munich Germany

12. Department of Experimental and Clinical Pharmacology; Medical University; Warsaw Poland

13. Medical Imaging Analysis Center AG; Basel Switzerland

Funder

Ministerstvo Zdravotnictví Ceské Republiky

Univerzita Karlova v Praze

Else Kröner-Fresenius-Stiftung

SFB TRR 43

Deutsche Forschungsgemeinschaft

Bundesministerium für Bildung und Forschung

Polish Ministry of Science and Higher Education

Publisher

Wiley

Subject

Physiology (medical),Clinical Neurology,Neurology,Histology,Pathology and Forensic Medicine

Reference61 articles.

1. Wilson's disease and other neurological copper disorders;Bandmann;Lancet Neurol,2015

2. Wilson's disease: a clinico-neuropathological autopsy study;Meenakshi-Sundaram;J Clin Neurosci,2008

3. The pallial component in hepato-lenticular degeneration;Richter;J Neuropathol Exp Neurol,1948

4. Wilson's disease: a case with almost total loss of white matter;Schulman;J Neuropathol Exp Neurol,1963

5. Neuropathological analysis of pathological forms of astroglia in Wilson's disease;Bertrand;Folia Neuropathol,2001

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