Changes in Airway Microbiome and Inflammation with Ivacaftor Treatment in Patients with Cystic Fibrosis and the G551D Mutation-Reference-Cited by-同舟云学术

Changes in Airway Microbiome and Inflammation with Ivacaftor Treatment in Patients with Cystic Fibrosis and the G551D Mutation

Published:2020-02 Issue:2 Volume:17 Page:212-220
ISSN:2329-6933
Container-title:Annals of the American Thoracic Society
language:en
Short-container-title:Annals ATS

Author:

Harris J. Kirk¹^ORCID,Wagner Brandie D.²^ORCID,Zemanick Edith T.¹^ORCID,Robertson Charles E.³^ORCID,Stevens Mark J.¹,Heltshe Sonya L.⁴^ORCID,Rowe Steven M.⁵^ORCID,Sagel Scott D.¹^ORCID

Affiliation:

1. Department of Pediatrics, Children's Hospital Colorado, and

2. Department of Biostatistics and Informatics, Colorado School of Public Health, University of Colorado Denver, Aurora, Colorado

3. Department of Medicine, University of Colorado School of Medicine, Aurora, Colorado

4. Department of Pediatrics, University of Washington, Seattle, Washington; and

5. Department of Medicine, Department of Pediatrics, and Department of Cell Developmental and Integrative Biology, University of Alabama at Birmingham, Birmingham, Alabama

Publisher

American Thoracic Society

Subject

Pulmonary and Respiratory Medicine

Link

https://www.atsjournals.org/doi/pdf/10.1513/AnnalsATS.201907-493OC

Reference18 articles.

1. A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation

2. Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with aG551DMutation

3. Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis

4. Impact of the CFTR-Potentiator Ivacaftor on Airway Microbiota in Cystic Fibrosis Patients Carrying A G551D Mutation

5. Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections

Cited by 123 articles. 订阅此论文施引文献订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献

1. Practical Guidance for Clinical Microbiology Laboratories: Updated guidance for processing respiratory tract samples from people with cystic fibrosis;Clinical Microbiology Reviews;2024-09-12

2. Metagenomics Applied to the Respiratory Mycobiome in Cystic Fibrosis;Mycopathologia;2024-09-12

3. Cystic fibrosis;Nature Reviews Disease Primers;2024-08-08

4. Efficacy and safety of LAU-7b in a Phase 2 trial in adults with cystic fibrosis;Journal of Cystic Fibrosis;2024-07

5. Quantifying abnormal alveolar microstructure in cystic fibrosis lung disease via hyperpolarized 129Xe diffusion MRI;Journal of Cystic Fibrosis;2024-07