Economic and social burden of cystic fibrosis in Poland. Estimates based on patients - reported data

Abstract

Cystic fibrosis (CF) is a genetic disease inherited as an autosomal recessive disorder. With an incidence of 1:2500 to 1:3000 in white race population it can be regarded as the most common rare disease. Taking into account clinical characteristics of patients, CF may place a substantial burden on a population both from social and economic point of view. The aim of the study was to estimate the cost of CF treatment in Poland with a special emphasis on outpatient treatment. Selected medical and social aspects were also investigated. Survey study was conducted on the sample of 100 children and adolescents patients. Indirect costs linked to lost productivity and a cost of care could be 4 fold higher then direct costs. Medication and diet costs are main components of direct costs. Life satisfaction is deteriorated in the vast majority of studied CF patients.