Disease-associated Mutations at Copper Ligand Histidine Residues of Superoxide Dismutase 1 Diminish the Binding of Copper and Compromise Dimer Stability-Reference-Cited by-同舟云学术

Disease-associated Mutations at Copper Ligand Histidine Residues of Superoxide Dismutase 1 Diminish the Binding of Copper and Compromise Dimer Stability

Published:2007-01 Issue:1 Volume:282 Page:345-352
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Wang Jiou,Caruano-Yzermans Amy,Rodriguez Angela,Scheurmann Jonathan P.,Slunt Hilda H.,Cao Xiaohang,Gitlin Jonathan,Hart P. John,Borchelt David R.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference48 articles.

1. Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

2. From charcot to lou gehrig: deciphering selective motor neuron death in als

3. Pathogenic superoxide dismutase structure, folding, aggregation and turnover

4. Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity.

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