The Endoplasmic Reticulum Degradation Pathway for Mutant Secretory Proteins α1-Antitrypsin Z and S Is Distinct from That for an Unassembled Membrane Protein-Reference-Cited by-同舟云学术

The Endoplasmic Reticulum Degradation Pathway for Mutant Secretory Proteins α1-Antitrypsin Z and S Is Distinct from That for an Unassembled Membrane Protein

Published:1996-05 Issue:22 Volume:271 Page:13215-13220
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Teckman Jeffrey H.,Perlmutter David H.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference30 articles.

1. Progress in Liver Disease;Perlmutter,1993

2. Risk of Cirrhosis and Primary Liver Cancer in Alpha1-Antitrypsin Deficiency

3. Alpha 1-antitrypsin deficiency, emphysema, and liver disease. Genetic basis and strategies for therapy.

4. Accumulation of PiZ alpha 1-antitrypsin causes liver damage in transgenic mice.

5. Neonatal Hepatitis Induced by α 1 -Antitrypsin: a Transgenic Mouse Model

Cited by 81 articles. 订阅此论文施引文献订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献

1. Biomarkers Associated With Future Severe Liver Disease in Children With Alpha-1-Antitrypsin Deficiency;Gastro Hep Advances;2024

2. Probing of the reactive center loop region of alpha-1-antitrypsin by mutagenesis predicts new type-2 dysfunctional variants;Cellular and Molecular Life Sciences;2023-12-13

3. Alpha-1 Antitrypsin Deficiency Liver Disease;Clinics in Liver Disease;2022-08

4. Human placental proteomics and exon variant studies link AAT/SERPINA1 with spontaneous preterm birth;BMC Medicine;2022-04-28

5. N‐glycan processing selects ERAD‐resistant misfolded proteins for ER‐to‐lysosome‐associated degradation;The EMBO Journal;2021-06-21