Frataxin Directly Stimulates Mitochondrial Cysteine Desulfurase by Exposing Substrate-binding Sites, and a Mutant Fe-S Cluster Scaffold Protein with Frataxin-bypassing Ability Acts Similarly-Reference-Cited by-同舟云学术

Frataxin Directly Stimulates Mitochondrial Cysteine Desulfurase by Exposing Substrate-binding Sites, and a Mutant Fe-S Cluster Scaffold Protein with Frataxin-bypassing Ability Acts Similarly

Published:2013-12 Issue:52 Volume:288 Page:36773-36786
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Pandey Alok,Gordon Donna M.,Pain Jayashree,Stemmler Timothy L.,Dancis Andrew,Pain Debkumar

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference41 articles.

1. Frataxin and mitochondrial Fe-S cluster biogenesis;Stemmler;J. Biol. Chem,2010

2. Biogenesis of iron-sulfur clusters in mammalian cells: new insights and relevance to human disease;Rouault;Dis. Model. Mech,2012

3. The role of mitochondria in cellular iron-sulfur protein biogenesis and iron metabolism;Lill;Biochim. Biophys. Acta,2012

4. Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion;Campuzano;Science,1996

5. Aconitase and mitochondrial iron-sulfur protein deficiency in Friedreich ataxia;Rötig;Nat. Genet,1997

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