A 7-kDa Prion Protein (PrP) Fragment, an Integral Component of the PrP Region Required for Infectivity, Is the Major Amyloid Protein in Gerstmann-Sträussler-Scheinker Disease A117V-Reference-Cited by-同舟云学术

A 7-kDa Prion Protein (PrP) Fragment, an Integral Component of the PrP Region Required for Infectivity, Is the Major Amyloid Protein in Gerstmann-Sträussler-Scheinker Disease A117V

Published:2001-02 Issue:8 Volume:276 Page:6009-6015
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Tagliavini Fabrizio,Lievens Patricia M.-J.,Tranchant Christine,Warter Jean-Marie,Mohr Michel,Giaccone Giorgio,Perini Francesco,Rossi Giacomina,Salmona Mario,Piccardo Pedro,Ghetti Bernardino,Beavis Ronald C.,Bugiani Orso,Frangione Blas,Prelli Frances

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference48 articles.

1. Über eine eigenartige hereditär- familiäre Erkrankung des Zentralnervensystems

2. Linkage of a prion protein missense variant to Gerstmann–Sträussler syndrome

3. Pro→Leu change at position 102 of prinon protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

4. A prion protein variant in a family with the telencephalic form of Gerstmann-Straussler-Scheinker syndrome

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