Mucopolysaccharidosis Type I, Unique Structure of Accumulated Heparan Sulfate and Increased N-Sulfotransferase Activity in Mice Lacking α-l-iduronidase-Reference-Cited by-同舟云学术

Mucopolysaccharidosis Type I, Unique Structure of Accumulated Heparan Sulfate and Increased N-Sulfotransferase Activity in Mice Lacking α-l-iduronidase

Published:2011-10 Issue:43 Volume:286 Page:37515-37524
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Holley Rebecca J.,Deligny Audrey,Wei Wei,Watson H. Angharad,Niñonuevo Milady R.,Dagälv Anders,Leary Julie A.,Bigger Brian W.,Kjellén Lena,Merry Catherine L.R.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference42 articles.

1. Prediction of neuropathology in mucopolysaccharidosis I patients

2. Cardiac Functional and Histopathologic Findings in Humans and Mice with Mucopolysaccharidosis Type I: Implications for Assessment of Therapeutic Interventions in Hurler Syndrome

3. Gross and Fine Motor Skills of Children with Hurler Syndrome (MPS-IH) Post Umbilical Cord Blood Transplantation: A Case Series Report

4. Mucopolysaccharidosis I: Management and Treatment Guidelines

5. Heparan sulphate proteoglycans fine-tune mammalian physiology

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