Neurodegeneration in Methylmalonic Aciduria Involves Inhibition of Complex II and the Tricarboxylic Acid Cycle, and Synergistically Acting Excitotoxicity-Reference-Cited by-同舟云学术

Neurodegeneration in Methylmalonic Aciduria Involves Inhibition of Complex II and the Tricarboxylic Acid Cycle, and Synergistically Acting Excitotoxicity

Published:2002-04 Issue:17 Volume:277 Page:14674-14680
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Okun Jürgen G.,Hörster Friederike,Farkas Lilla M.,Feyh Patrik,Hinz Angela,Sauer Sven,Hoffmann Georg F.,Unsicker Klaus,Mayatepek Ertan,Kölker Stefan

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference47 articles.

1. The Metabolic and Molecular Bases of Inherited Disease;Fenton,2001

2. Methylmalonicacidemia: biochemical heterogeneity in defects of 5'-deoxyadenosylcobalamin synthesis.

3. The Natural History of the Inherited Methylmalonic Acidemias

4. Clinical outcome of long-term management of patients with vitamin B12-unresponsive methylmalonic acidemia

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